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ArtículoDerechos de autor
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Fecha del embargo
2020-07-10
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- INI - Artigos de Periódicos [3393]
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IDIOPATHIC HISTIOCYTOID SWEET SYNDROME: A CASE REPORT WITH CLINICAL AND HISTOPATHOLOGICAL CONSIDERATIONS
Autor
Afiliación
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Department of Family Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Department of Pathology. Rio de Janeiro, RJ, Brazil
Incentive to Research Fund Association. São Paulo, SP, Brazil.
Municipal Healthy Department. Residency Program in Family and Community Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Department of Pathology. Rio de Janeiro, RJ, Brazil
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Department of Family Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Department of Pathology. Rio de Janeiro, RJ, Brazil
Incentive to Research Fund Association. São Paulo, SP, Brazil.
Municipal Healthy Department. Residency Program in Family and Community Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Post Graduation Course. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Department of Pathology. Rio de Janeiro, RJ, Brazil
Resumen en ingles
Background: Histiocytoid Sweet syndrome is characterized by a predominant neutrophilicdermal infiltrate. Usual clinical differential diagnosis includes erythema multiforme, drugeruption, and erythema nodosum. Histiocytoid Sweet syndrome is considered anuncommon histopathological variant of the disease.Methods: We evaluated clinical, histopathological, and immunohistochemical findings of acase categorized as idiopathic histiocytoid Sweet syndrome in which clinical-epidemiological data raised the possibilities of Sweet syndrome, leprosy, and drug reaction.Results: Positive reaction to myeloperoxidase (MPO) in histiocytoid cells of the dermalinfiltrate, response to oral corticosteroids, clinical and laboratory investigation, and absenceof cutaneous lesions or clinical complaints within 1 year of follow-up are consistent with thediagnosis of idiopathic histiocytoid Sweet syndrome. CD68 (PG-M1) and CD15 positivecells were also present among dermal cells. Conclusions: Epidemiological data are relevant while considering a clinical differentialdiagnosis of Sweet syndrome that can be further expanded, from a histopathological pointof view, when dealing with the histiocytoid variant since neutrophils, macrophages, andimmature myelomonocytic cells with histiocytoid morphology are present. The significanceof the MPO positive mononuclear dermal cells are not completely established.
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