Author | Medeiros Junior, Manoel | |
Author | Araujo, Maria Ilma | |
Author | Guimarães, Newton Sales | |
Author | Freitas, Luiz Antonio Rodrigues de | |
Author | Silva, Tânia Maria Correia | |
Author | Carvalho Filho, Edgar Marcelino | |
Access date | 2014-07-09T19:06:09Z | |
Available date | 2014-07-09T19:06:09Z | |
Document date | 2002 | |
Citation | MEDEIROS JUNIOR, M. et al. Therapeutic response to thalidomide in Melkersson-Rosenthal syndrome: a case report. Annals of Allergy, Asthma and Immunology, v. 88, n. 4, p. 421-424, 2002. | pt_BR |
ISSN | 1081-1206 | |
URI | https://www.arca.fiocruz.br/handle/icict/7896 | |
Language | eng | pt_BR |
Publisher | Elsevier | pt_BR |
Rights | open access | pt_BR |
Title | Therapeutic response to thalidomide in Melkersson-Rosenthal syndrome: a case report. | pt_BR |
Type | Article | pt_BR |
Abstract | BACKGROUND: Melkersson-Rosenthal syndrome (MRS) is a rare disorder of unknown etiology characterized by a triad of symptoms: recurrent orofacial swelling, relapsing facial palsy. and a fissured tongue. A differential diagnosis must be made with other granulomatous diseases, such as sarcoidosis and oral Crohn disease; however, the histologic findings of noncaseating, sarcoidal granulomas support the diagnosis of MRS. RESULTS: Many therapeutic modalities have been described for this disease. In this case report, we present a patient with MRS that was treated with thalidomide because of the identification of tumor necrosis factor a in the lesion by immunohistochemical analysis. This is the first reported detection of tumor necrosis factor a in an MRS lesion, as well the first reported use of thalidomide to treat this clinical condition | pt_BR |
Affilliation | Hospital Universitário Professor Edgard Santos. Universidade Federal da Bahia. Serviço de Imunologia. Salvador, BA, Brasil | pt_BR |
Affilliation | Hospital Universitário Professor Edgard Santos. Universidade Federal da Bahia. Serviço de Imunologia. Salvador, BA, Brasil | pt_BR |
Affilliation | Universidade Federal da Bahia. Division of Dermatology. Salvador, BA, Brasil | pt_BR |
Affilliation | Fundação Oswaldo Cruz. Centro de Pesquisa Gonçalo Moniz. Laboratório de Patologia e Biologia Molecular. Salvador, BA, Brasil / Universidade Federal da Bahia. Faculdade de Medicina da Bahia. Salvador, BA, Brasil / Escola Baiana de Medicina e Saúde Pública. Salvador, BA, Brasil | pt_BR |
DeCS | Imunossupressores/uso terapêutico | pt_BR |
DeCS | Síndrome de Melkersson-Rosenthal/quimioterapia | pt_BR |
DeCS | Talidomida/uso terapêutico | pt_BR |
DeCS | Fator de Necrose Tumoral alfa/antagonistas & inibidores | pt_BR |
DeCS | Adolescente | pt_BR |
DeCS | Anti-Inflamatórios/administração & dosagem | pt_BR |
DeCS | Anti-Inflamatórios/uso terapêutico | pt_BR |
DeCS | Biópsia | pt_BR |
DeCS | Dexametasona/administração & dosagem | pt_BR |
DeCS | Dexametasona/uso terapêutico | pt_BR |
DeCS | Quimioterapia Combinada | pt_BR |
DeCS | Humanos | pt_BR |
DeCS | Quimioterapia Combinada | pt_BR |
DeCS | Lábio/química | pt_BR |
DeCS | Masculino | pt_BR |
DeCS | Síndrome de Melkersson-Rosenthal/metabolismo | pt_BR |
DeCS | Indução de Remissão | pt_BR |
DeCS | Talidomida/administração & dosagem | pt_BR |
DeCS | Fator de Necrose Tumoral alfa/análise | pt_BR |