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PRENATAL DIAGNOSIS OF PENTALOGY OF CANTRELL IN THE FIRST TRIMESTER: IS 3-DIMENSIONAL SONOGRAPHY NEEDED?
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Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Obstetrícia. Unidade de Medicina Fetal. Rio de Janeiro, RJ, Brasil.
Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Obstetrícia. Unidade de Medicina Fetal. Rio de Janeiro, RJ, Brasil.
Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Obstetrícia. Unidade de Medicina Fetal. Rio de Janeiro, RJ, Brasil.
Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Obstetrícia. Unidade de Medicina Fetal. Rio de Janeiro, RJ, Brasil.
Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Obstetrícia. Unidade de Medicina Fetal. Rio de Janeiro, RJ, Brasil.
Abstract
We report the prenatal diagnosis of 2
cases of Pentalogy of Cantrell in the first trimester. In
case 1, sonographic evaluation revealed ectopia cor-dis, omphalocele, and cystic hygroma at 10 weeks’
gestation. In case 2, sonographic assessment during
the first trimester detected ectopia cordis and ompha-locele at 11 weeks’ gestation. In both cases, the
patient opted for elective pregnancy termination, and
Pentalogy of Cantrell was confirmed in 2 male
fetuses. We discuss the role of Doppler imaging and
3-dimensional sonography as complementary meth-ods to conventional sonographic assessment of ab-dominal wall defects at early pregnancy.
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