| Author | Salomão, José Francisco Manganelli | |
| Author | Bellas, Antônio R. | |
| Author | Leibinger, Renê D. | |
| Author | Barbosa, Ana Paula A. | |
| Author | Brandão, Maria Anna P. B. | |
| Access date | 2013-03-05T14:58:45Z | |
| Available date | 2013-03-05T14:58:45Z | |
| Document date | 1998 | |
| Citation | SALOMÃO, José Francisco Manganelli et al. Malformação de chiari do tipo II sintomática. Arquivos de Neuro-Psiquiatria, São Paulo, v. 56, n. 1, p. 98-106, Mar. 1998. | pt_BR |
| ISSN | 0004-282X | |
| URI | https://www.arca.fiocruz.br/handle/icict/6347 | |
| Abstract in Portuguese | Os autores analisam uma série de 17 crianças portadoras de mielodisplasias que desenvolveram sinais e sintomas da malformação de Chiari do tipo II. De acordo com a idade, dois grupos ficaram bem definidos: Grupo I, crianças no primeiro ano de vida, em que predominaram sinais e sintomas de comprometimento do tronco encefálico e nervos cranianos bulbares (n=13); Grupo II, composto por crianças com idade superior a um ano, em que as principais manifestações foram dor cervical e sinais cerebelares (n=4). O resultado do tratamento cirúrgico nos dois grupos foi distinto: enquanto a mortalidade no Grupo I atingiu 46,1%, nenhum paciente do Grupo II veio a falecer. O tratamento inicial consistiu na instalação ou revisão de derivação ventricular, sendo a descompressão crânio-vertebral reservada àqueles que não se beneficiaram com esses procedimentos. Os autores enfatizam a necessidade do imediato reconhecimento e tratamento do quadro, de modo a se obter resultados satisfatórios. | pt_BR |
| Language | por | pt_BR |
| Publisher | Academia Brasileira de Neurologia | pt_BR |
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| Rights | open access | |
| Subject in Portuguese | Mielomeningocele | pt_BR |
| Subject in Portuguese | Malformação de Chiari do Tipo II | pt_BR |
| Subject in Portuguese | Malformação de Arnold-Chiari | pt_BR |
| Subject in Portuguese | Desconpressão de Fossa Craniana Posterior | pt_BR |
| Subject in Portuguese | Hidrocefalia | pt_BR |
| Subject in Portuguese | Paralisia de Cordas Vocais | pt_BR |
| Title | Malformação de chiari do tipo II sintomática | pt_BR |
| Alternative title | Symptomatic Chiari type II malformation | |
| Type | Article | pt_BR |
| DOI | 10.1590/S0004-282X1998000100016 | pt_BR |
| Abstract | The Chiari type II malformation is the leading cause of death in infants with myelomeningocele. The authors report 17 cases of symptomatic Chiari type II malformation occurring in two distinct age dependent population. In Group I, 13 neonates and infants in the first year of life presented with cranial nerve and brain stem dysfunction characterized by vocal cord paralysis, apnea, dysphagia and laryngeal stridor. In Group II, 4 patients developed signs and symptoms after the first year of life. In this group, the presentation was more insidious and included neck pain and cerebellar manifestations. The surgical treatment consisted initially in shunt implantation or revision and when there was no improvement, posterior fossa decompression was performed. The response to the surgical treatment differed considerably between the two groups: older patients improved promptly after surgery and there was no casualties; in newborn and infants, especially those under 6 months of age, the mortality rate was 46.1%. The authors stress that prompt diagnosis and surgical intervention should be performed in order to produce a favorable outcome. | pt_BR |
| Affilliation | Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Cirurgia Pediátrica. Serviço de Neurocirurgia Pediátrica. Rio de Janeiro, RJ, Brasil. | pt_BR |
| Affilliation | Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Cirurgia Pediátrica. Serviço de Neurocirurgia Pediátrica. Rio de Janeiro, RJ, Brasil. | pt_BR |
| Affilliation | Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Cirurgia Pediátrica. Serviço de Neurocirurgia Pediátrica. Rio de Janeiro, RJ, Brasil. | pt_BR |
| Affilliation | Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Cirurgia Pediátrica. Serviço de Neurocirurgia Pediátrica. Rio de Janeiro, RJ, Brasil. | pt_BR |
| Affilliation | Fundação Oswaldo Cruz. Instituto Fernandes Figueira. Departamento de Cirurgia Pediátrica. Serviço de Neurocirurgia Pediátrica. Rio de Janeiro, RJ, Brasil. | pt_BR |
| Subject | Myelomeningocele | pt_BR |
| Subject | Chiari type II Malformation | pt_BR |
| Subject | Arnold-Chiari Malformation | pt_BR |
| Subject | Posterior Fossa Decompression | pt_BR |
| Subject | Hydrocephalus | pt_BR |
| Subject | Vocal Cord Paralysis | pt_BR |
