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https://www.arca.fiocruz.br/handle/icict/34890
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ArticleCopyright
Open access
Embargo date
2020-08-20
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- INI - Artigos de Periódicos [3646]
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CYLINDROMA: AN UPDATE
Affilliation
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Pathology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Pathology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Federal University of Rio de Janeiro. University Hospital. Sector of Dermatology. Rio de Janeiro, RJ, Brazil / Federal University of Rio de Janeiro. School of Medicine. Rio de Janeiro, RJ, Brazil.
Abstract
This paper reviews the recent literature on cylindroma, a rare tumor originating from the cutaneous adnexal structures of the scalp and face. Benign cylindroma is more frequent in women, and there are solitary and multiple forms, which are autosomal. Malignant cylindroma can occur in the Brooke–Spiegler syndrome, and malignant transformation is more frequent in multiple variants than in solitary tumors. Its histopathological basis is controversial, and its origin is unknown, although it is known that there is a genetic basis for onset of these tumors in Brooke-Spiegler syndrome.
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